Superficial siderosis of the CNS associated with multiple cavernous malformations.
نویسندگان
چکیده
Superficial siderosis of the CNS due to chronic, recurrent subarachnoid hemorrhage is an uncommon and potentially debilitating disorder. The classic clinical manifestation is progressive bilateral sensorineural hearing loss (SNHL), although ataxia and pyramidal signs also are observed frequently. Cavernous malformations rarely present with subarachnoid hemorrhage. We describe an unusual case of a young patient who presented with progressive, bilateral SNHL who was found to have superficial CNS siderosis associated with multiple cavernous malformations.
منابع مشابه
Intradural extramedullary cavernous malformation with extensive superficial siderosis of the neuraxis: Case report and review of literature
BACKGROUND Spinal cavernous malformations usually affect the vertebral bodies and are seldom intradural. Here, we report a rare spinal intradural-extramedullary cavernous malformation associated with extensive superficial siderosis along the neuraxis in a patient with radicular complaints. CASE DESCRIPTION A 60-year-old male presented with subacute headaches, intermittent fever, and acute bac...
متن کاملSuperficial siderosis of the central nervous system: an unusual cause of sensorineural hearing loss.
Neurology Service, State University of Rio de Janeiro (UERJ), Rio de Janeiro RJ, Brazil; Laboratory of Panic & Respiration, Institute of Psychiatry, Federal University of Rio de Janeiro (UFRJ), INCT Translational Medicine, Rio de Janeiro RJ, Brazil. Superficial siderosis (SS) of the central nervous system (CNS) is a rare disorder characterized by a classic triad of symptoms consisting of sensor...
متن کاملErratum: Rare association of secondary superficial siderosis caused by a fourth ventricle hemorrhagic ependymoma mimicking a cavernoma: Case report and literature review
[This corrects the article on p. 14 in vol. 8, PMID: 28217393.].
متن کاملSuperficial siderosis of the central nervous system.
We report five cases of superficial siderosis of the central nervous system. All patients developed progressive deafness and cerebellar ataxia associated with pyramidal tract signs or mental deterioration. The cerebrospinal fluid examinations usually revealed an elevated protein level, without other abnormalities. Magnetic resonance imaging typically showed a hypointense rim around the cerebral...
متن کاملIntracranial dural arteriovenous fistula as a cause for symptomatic superficial siderosis: A report of two cases and review of the literature
BACKGROUND Superficial siderosis (SS) is the occult deposition of hemosiderin within the cerebral cortex due to repeat microhemorrhages within the central nervous system. The collection of hemosiderin within the pia and superficial cortical surface can lead to injury to the nervous tissue. The most common presentation is occult sensorineural hearing loss although many patients have been misdiag...
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عنوان ژورنال:
- AJNR. American journal of neuroradiology
دوره 20 7 شماره
صفحات -
تاریخ انتشار 1999